Browsing by Author Weatherall, D.J.

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Issue DateTitleAuthor(s)
2007Age-related changes in adaptation to severe anemia in childhood in developing countriesO Donnell, A.; Premawardhena, A.; Arambepola, M.; Allen, S.J.; Peto, T.E.; Fisher, C.A.; Rees, D.C.; Olivieri, N.F.; Weatherall, D.J.
2007Cardiac functions in older patients with haemoglobin E- β thalassaemiaPremawardhena, A.P.; Wanninayake, S.; Dolapihilla, S.N.; Kapuruge, L.; Katugaha, N.; Olivieri, N.F.; Weatherall, D.J.
2013Chracterisation of beta giobin mutations in Sri Lankan patients with betathalassaemia intermediaPerera, S.; Silva, D.P.S.I.; Hapugoda, M.; Wickramarathne, M.N.; Wijesirwardhena, I.; Efremove, D.G.; Fisher, C.A.; Weatherall, D.J.; Premawardhena, A.P.
2015Clinical and molecular heterogeneity among Beta Thalassaemia Intermedia in Sri LankaPerera, P.S.; Silva, D.P.S.I.; Hapugoda, M.; Wickramarathne, M.N.; Wijesiriwardena, I.; Efremov, D.G.; Fisher, C.A.; Weatherall, D.J.; Premawardhena, A.
2003The clinical effects of excessive a globin genes : two family studiesPremawardhena, A.P.; Fisher, C.A.; Rugless, M.; de Silva, S.; Perera, A.W.V.S.; Olivien, N.F.; Weatherall, D.J.
2015Correlation of genotype with phenotype in beta thalassaemia intermedia in Sri lankaPerera, P.S.; Silva, D.P.S.I.; Hapugoda, M.; Wickramarathne, M.N.; Wijesiriwardena, I.; Efremov, D.G.; Fisher, C.A.; Weatherall, D.J.; Premawardhena, A.
2011A Functional element necessary for fetal hemoglobin silencingSankaran, V.G.; Xu, J.; Byron, R.; Greisman, H.A.; Fisher, C.; Weatherall, D.J.; Sabath, D.E.; Groudine, M.; Orkin, S.H.; Premawardhena, A.; Bender, M.A.
2001Genetic determinants of jaundice and gallstones in haemoglobin E beta thalassaemiaPremawardhena, A.P.; Fisher, C.A.; Fathihu, F.; de Silva, S.; Perera, W.; Peto, T.E.; Olivieri, N.F.; Weatherall, D.J.
2019Genotype-phenotype association analysis identifies the role of α globin genes in modulating disease severity of β thalassaemia intermedia in Sri LankaPerera, S.; Allen, A.; Silva, I.; Hapugoda, M.; Wickramarathne, M.N.; Wijesiriwardena, I.; Allen, S.; Rees, D.; Efremov, D.G.; Fisher, C.A.; Weatherall, D.J.; Premawardhena, A.
2003The Global distribution of length polymorphisms of the promoters of the gucuronosyltransferase I gene(UGTIAI): hematologic and evolutionary implicationsPremawardhena, A.P.; Fisher, C.A.; Liu, Y.T.; Verma, I.C.; de Silva, S.; Arambepola, M.; Clegg, J.B.; Weatherall, D.J.
2005Haemoglobin E beta thalassaemia in Sri LankaPremawardhena, A.; Fisher, C.A.; Olivieri, N.F.; de Silva, S.; Arambepola, M.; Perera, W.; O Donnell, A.; Peto, T.E.; Viprakasit, V.; Merson, L.; Muraca, G.; Weatherall, D.J.
2018Haemoglobin variants, iron status and anaemia in Sri Lankan adolescents with low red cell indices: A cross sectional surveyRodrigo, R.; Allen, A.; Manamperi, A.; Perera, L.; Fisher, C.A.; Allen, S.; Weatherall, D.J.; Premawardhena, A.
2005Hemoglobin E-beta-thalassemia: Progress report from the international study groupPremawardhena, A.; de Silver, S.; Arambepola, M.; Olivieri, N.F.; Vichinsky, E.P.; Merson, L.; Muraco, G.; Allen, A.; Fisher, C.; Peto, T.; Weatherall, D.J.
2017Hepcidin detects iron deficiency in Sri Lankan adolescents with a high burden of hemoglobinopathy: A diagnostic test accuracy studyWray, K.; Allen, A.; Evans, E.; Fisher, C.; Premawardhena, A.; Perera, L.; Rodrigo, R.; Goonathilaka, G.; Ramees, L.; Webster, C.; Armitage, A.E.; Prentice, A.M.; Weatherall, D.J.; Drakesmith, H.; Pasricha, S.R.
2015Hepcidin is suppressed by erythropoiesis in hemoglobin E β-thalassemia and β-thalassemia traitJones, E.; Pasricha, S.R.; Allen, A.; Evans, P.; Fisher, C.A.; Wray, K.; Premawardhena, A.; Bandara, D.; Perera, A.; Webster, C.; Sturges, P.; Olivieri, N.F.; St Pierre, T.; Armitage, A.E.; Porter, J.B.; Weatherall, D.J.; Drakesmith, H.
1999Impact of a low transfusion regimen on growth and iron loading in haemoglobin E/beta thalassaemiaOlivieri, N.F.; Sharma S.; de Silva, S.; Premawardhena, A.P.; Viens, A.M.; Taylor, C.M.; Symes, K.N.; Vichinsky, E.P.; Brittenham, G.M.; Weatherall, D.J.
2009Interaction of malaria with a common form of severe thalassemia in an Asian populationO Donnell, A.; Premawardhena, A.; Arambepola, M.; Samaranayake, R.; Allen, S.J.; Peto, T.E.; Fisher, C.A.; Cook, J.; Corran, P.H.; Olivieri, N.F.; Weatherall, D.J.
2000Iron overload and iron-chelating therapy in haemoglobin E/beta thalassaemiaOlivieri, N.F.; de Silva, S.; Premawardhena, A.P.; Sharma S.; Viens, A.M.; Taylor, C.M.; Brittenham, G.M.; Weatherall, D.J.
2009Iron overload in the Asian communityLok, C.Y.; Merryweather-Clarke, A.T.; Viprakasit, V.; Chinthammitr, Y.; Srichairatanakool, S.; Limwongse, C.; Oleesky, D.; Robins, A.J.; Hudson, J.; Wai, P.; Premawardhena, A.; de Silva, H.J.; Dassanayake, A.S.; McKeown, C.; Jackson, M.; Gama, R.; Khan, N.; Newman, W.; Banait, G.; Chilton, A.; Wilson-Morkeh, I.; Weatherall, D.J.; Robson, K.J.H.
2017Iron status and anaemia in Sri Lankan secondary school children: A cross-sectional surveyAllen, A.; Allen, S.; Rodrigo, R.; Perera, L.; Shao, W.; Li, C.; Wang, D.; Oliviery, N.; Weatherall, D.J.; Premawardhena, A.P.