de Silva, D.G.H.Devasiri, I.V.Dharmasiri, H.Pathirana, C.2014-10-292014-10-291995The Ceylon Medical Journal. 1995; 40(1): pp.40-410009-0875 (Print)http://repository.kln.ac.lk/handle/123456789/1247Indexed in MEDLINEA six week old baby girl from a closed Malay community in Hambantota presented with gradually increasing oedema since two weeks of age. She was oedematous, with gross non selective proteinuria, hypoproteinaemia and hypercholesterolaemaia. Congenital nephrotic syndrome is extremely rare and has not been reported previously in Sri LankaNephrotic Syndrome-congenitalCase ReportPaediatrics