Browsing by Author Weatherall, D.J.

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Issue DateTitleAuthor(s)
2005Haemoglobin E beta thalassaemia in Sri LankaPremawardhena, A.; Fisher, C.A.; Olivieri, N.F.; de Silva, S.; Arambepola, M.; Perera, W.; O Donnell, A.; Peto, T.E.; Viprakasit, V.; Merson, L.; Muraca, G.; Weatherall, D.J.
2018Haemoglobin variants, iron status and anaemia in Sri Lankan adolescents with low red cell indices: A cross sectional surveyRodrigo, R.; Allen, A.; Manamperi, A.; Perera, L.; Fisher, C.A.; Allen, S.; Weatherall, D.J.; Premawardhena, A.
2005Hemoglobin E-beta-thalassemia: Progress report from the international study groupPremawardhena, A.; de Silver, S.; Arambepola, M.; Olivieri, N.F.; Vichinsky, E.P.; Merson, L.; Muraco, G.; Allen, A.; Fisher, C.; Peto, T.; Weatherall, D.J.
2017Hepcidin detects iron deficiency in Sri Lankan adolescents with a high burden of hemoglobinopathy: A diagnostic test accuracy studyWray, K.; Allen, A.; Evans, E.; Fisher, C.; Premawardhena, A.; Perera, L.; Rodrigo, R.; Goonathilaka, G.; Ramees, L.; Webster, C.; Armitage, A.E.; Prentice, A.M.; Weatherall, D.J.; Drakesmith, H.; Pasricha, S.R.
2015Hepcidin is suppressed by erythropoiesis in hemoglobin E β-thalassemia and β-thalassemia traitJones, E.; Pasricha, S.R.; Allen, A.; Evans, P.; Fisher, C.A.; Wray, K.; Premawardhena, A.; Bandara, D.; Perera, A.; Webster, C.; Sturges, P.; Olivieri, N.F.; St Pierre, T.; Armitage, A.E.; Porter, J.B.; Weatherall, D.J.; Drakesmith, H.
1999Impact of a low transfusion regimen on growth and iron loading in haemoglobin E/beta thalassaemiaOlivieri, N.F.; Sharma S.; de Silva, S.; Premawardhena, A.P.; Viens, A.M.; Taylor, C.M.; Symes, K.N.; Vichinsky, E.P.; Brittenham, G.M.; Weatherall, D.J.
2009Interaction of malaria with a common form of severe thalassemia in an Asian populationO Donnell, A.; Premawardhena, A.; Arambepola, M.; Samaranayake, R.; Allen, S.J.; Peto, T.E.; Fisher, C.A.; Cook, J.; Corran, P.H.; Olivieri, N.F.; Weatherall, D.J.
2000Iron overload and iron-chelating therapy in haemoglobin E/beta thalassaemiaOlivieri, N.F.; de Silva, S.; Premawardhena, A.P.; Sharma S.; Viens, A.M.; Taylor, C.M.; Brittenham, G.M.; Weatherall, D.J.
2009Iron overload in the Asian communityLok, C.Y.; Merryweather-Clarke, A.T.; Viprakasit, V.; Chinthammitr, Y.; Srichairatanakool, S.; Limwongse, C.; Oleesky, D.; Robins, A.J.; Hudson, J.; Wai, P.; Premawardhena, A.; de Silva, H.J.; Dassanayake, A.S.; McKeown, C.; Jackson, M.; Gama, R.; Khan, N.; Newman, W.; Banait, G.; Chilton, A.; Wilson-Morkeh, I.; Weatherall, D.J.; Robson, K.J.H.
2017Iron status and anaemia in Sri Lankan secondary school children: A cross-sectional surveyAllen, A.; Allen, S.; Rodrigo, R.; Perera, L.; Shao, W.; Li, C.; Wang, D.; Oliviery, N.; Weatherall, D.J.; Premawardhena, A.P.
2017An islandwide hospital based epidemiological survey of haemoglobinopathies and an assessment of standards of care in 23 centresPremawardhena, A.P.; Mudiyanse, R.M.; Jifri, M.N.; Nelumdeniya, U.B.P.; Silva, D.P.S.I.; Nizri, A.H.M.; Rajiyah, M.O.F.; de Silva, T.U.N.; Pushpakumara, K.R.C.; Dissanayake, D.M.R.; Jansz, M.; Rifaya, M.I.; Navarathne, N.M.U.S.B.; Arambepola, W.W.M.M.; Thirukumaran, V.; Mendis, D.; Weerasekara, K.P.; de Silva, N.N.; Vaidyanatha, U.S.de.S.; Mettananda, D.S.G.; Oliveri, N.F.; Weatherall, D.J.
2022Leg ulcers: A report in patients with hemoglobin E beta thalassemia and review of the literature in severe beta ThalassemiaMehta, V.; Kirubarajan, A.; Sabouhanian, A.; Jayawardena, S.M.; Chandrakumaran, P.; Thangavelu, N.; Cader, R.; Mettananda, S.; Bandara, D.; Khan, S.; Weatherall, D.J.; Allen, A.; Premawardhena, A.P.; Olivieri, N.F.
2020Marriage patterns in Sri Lanka and the prevalence of parental consanguinity in patients with β-thalassaemia: a cross-sectional descriptive analysisPremawardhena, A.P.; de Silva, S.T.; Goonatilleke, M.D.D.C.; Ediriweera, D.S.; Mettananda, S.; Rodrigo, B.K.R.P.; Allen, A.; Weatherall, D.J.
2014Micro mapping of common alpha thalassaemia deletions (3.7 kb, 4.2 kb) in Sri Lanka and assessment of the contribution of alpha thalassemia to hypochromic microcytosisRodriao, B.K.R.P.; Perera, H.L.; Branava, U.; Manamperi, A.A.P.S.; Weatherall, D.J.; Premawardhena, A.P.
2003The Molecular basis for the thalassaemias in Sri LankaFisher, C.A.; Premawardhena, A.P.; de Silva, S.; Perera, G.; Rajapaksa, S.; Olivieri, N.A.; Old, J.M.; Weatherall, D.J.; Sri Lanka Thalassaemia Study Group
2005A Novel molecular basis for beta thalassemia intermedia poses new questions about its pathophysiologyPremawardhena, A.; Fisher, C.A.; Olivieri, N.F.; de Silva, S.; Sloane-Stanley, J.; Wood, W.G.; Weatherall, D.J.
2004Paraspinal extramcduallry erythropoiesis- a rare cause of spinal cord compression: two case reportsArambepola, M.; Premawardhena, A.P.; de Silva, S.; Olivieri, N.; Weatherall, D.J.
2015Rare hemoglobin variants: Hb G-Szuhu (HBB: c.243C>G), Hb G-Coushatta (HBB: c.68A>C) and Hb Mizuho (HBB:c.206T>C) in Sri Lankan familiesPerera, P.S.; Silva, I.; Hapugoda, M.; Wickramarathne, M.N.; Wijesiriwardena, I.; Efremov, D.G.; Fisher, C.A.; Weatherall, D.J.; Premawardhena, A.
2004Response of jaundice to phenobarbitone in thalassaemic patients co-inheriting Gilbert syndromePremawardhena, A.P.; Arambepola, M.; Fisher, C.A.; Oliveiri, N.F.; Weatherall, D.J.
2016“Silent” white matter changes in brain MRI in patients with haemoglobinopathies and their clinical significancePremawardhena, A.P.; Ranawaka, U.R.; Hapangama, A.; Pathmeswaran, A.; Hettiarachchi, S.; Salvin, K.A.; Pilapitiya, T.; Sanjaya, G.; Oilvieri, N.F.; Weatherall, D.J.